SGSH Rabbit Polyclonal Antibody (CAB8148)
- SKU:
- CAB8148
- Product Type:
- Antibody
- Applications:
- WB
- IHC
- Reactivity:
- Human
- Mouse
- Rat
- Host Species:
- Rabbit
- Isotype:
- IgG
- Research Area:
- Cell Biology
Frequently bought together:
Description
Product Name: | SGSH Rabbit Polyclonal Antibody |
SKU: | CAB8148 |
Size: | 20uL, 100uL |
Isotype: | IgG |
Host Species: | Rabbit |
Reactivity: | Human,Mouse,Rat |
Immunogen: | Recombinant fusion protein containing a sequence corresponding to amino acids 273-502 of human SGSH (NP_000190.1). |
Sequence: | DNGI PFPS GRTN LYWP GTAE PLLV SSPE HPKR WGQV SEAY VSLL DLTP TILD WFSI PYPS YAIF GSKT IHLT GRSL LPAL EAEP LWAT VFGS QSHH EVTM SYPM RSVQ HRHF RLVH NLNF KMPF PIDQ DFYV SPTF QDLL NRTT AGQP TGWY KDLR HYYY RARW ELYD RSRD PHET QNLA TDPR FAQL LEML RDQL AKWQ WETH DPWV CAPD GVLE EKLS PQCQ PLHN EL |
Tested Applications: | WB ELISA |
Recommended Dilution: | WB,1:100 - 1:500 |
Synonyms: | HSS; SFMD; MPS3A; SGSH |
Positive Sample: | Mouse lung |
Conjugate: | Unconjugated |
Cellular Localization: | Lysosome. |
Calculated MW: | 57kDa |
Observed MW: | 57kDa |
This gene encodes the enzyme sulfamidase; one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
Purification Method: | Affinity purification |
Gene ID: | 6448 |
Storage Buffer: | Store at -20℃. Avoid freeze / thaw cycles.Buffer: PBS with 0.02% sodium azide,50% glycerol,pH7.3. |