beta glucuronidase (GUSB) Rabbit Monoclonal Antibody (CAB19248)
- SKU:
- CAB19248
- Product Type:
- Antibody
- Antibody Type:
- Monoclonal Antibody
- Reactivity:
- Human
- Host Species:
- Rabbit
- Isotype:
- IgG
- Synonyms:
- GUSB
- BG
- MPS7
- beta-glucuronidase
- Research Area:
- Cell Biology
Frequently bought together:
Description
Product Name: | beta glucuronidase (GUSB) Rabbit Monoclonal Antibody |
SKU: | CAB19248 |
Size: | 20uL, 100uL |
Isotype: | IgG |
Host Species: | Rabbit |
Reactivity: | Human |
Immunogen: | A synthetic peptide corresponding to a sequence within amino acids 1-100 of human beta glucuronidase (GUSB) (NP_000172.2). |
Sequence: | MARG SAVA WAAL GPLL WGCA LGLQ GGML YPQE SPSR ECKE LDGL WSFR ADFS DNRR RGFE EQWY RRPL WESG PTVD MPVP SSFN DISQ DWRL RHFV GWVW |
Tested Applications: | WB ELISA |
Recommended Dilution: | WB,1:500 - 1:1000 |
Synonyms: | BG; MPS7; beta glucuronidase (GUSB) |
Positive Sample: | HepG2,A-549,HL-60 |
Conjugate: | Unconjugated |
Cellular Localization: | Lysosome. |
Calculated MW: | 75kDa |
Observed MW: | 75kDa |
This gene encodes a hydrolase that degrades glycosaminoglycans, including heparan sulfate, dermatan sulfate, and chondroitin-4,6-sulfate. The enzyme forms a homotetramer that is localized to the lysosome. Mutations in this gene result in mucopolysaccharidosis type VII. Alternative splicing results in multiple transcript variants. There are many pseudogenes of this locus in the human genome.
Purification Method: | Affinity purification |
Gene ID: | 2990 |
Clone Number: | ARC2408 |
Storage Buffer: | Store at -20℃. Avoid freeze / thaw cycles.Buffer: PBS with 0.02% sodium azide,0.05% BSA,50% glycerol,pH7.3. |